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Staged Single Ventricle Palliation and Homozygous Sickle Cell Disease
Author(s) -
Maddali Madan Mohan,
Junghare Minakshi Sandip,
Nishant Arora Ram,
Kandachar Pranav Subbaraya,
Valliattu Johan
Publication year - 2016
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/jocs.12721
Subject(s) - medicine , ventricle , hypoxemia , fontan procedure , disease , cardiology , palliative care , hypoxia (environmental) , surgery , oxygen , chemistry , nursing , organic chemistry
Hypoxemia is a well‐known trigger for precipitating a sickling crisis in patients with sickle cell disease. Patients undergoing staged single ventricle palliation have hypoxemia during the initial stages of the Fontan pathway. The successful completion of staged single ventricle palliation in a child with a combination of homozygous sickle cell disease and a single ventricle physiology that tolerate prolonged hypoxemia during earlier stages of Fontan pathway is described. doi: 10.1111/jocs.12721 (J Card Surg 2016;31:237–241)