
Renal Fibromuscular Dysplasia: A Not So Common Entity of Secondary Hypertension
Author(s) -
Sanidas Elias A.,
Seferou Maria,
Papadopoulos Dimitris P.,
Makris Anastasios,
Viniou Nora A.,
Chantziara Vasiliki,
Cennimata Vasiliki,
Papademetriou Vasilios
Publication year - 2016
Publication title -
the journal of clinical hypertension
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.909
H-Index - 67
eISSN - 1751-7176
pISSN - 1524-6175
DOI - 10.1111/jch.12650
Subject(s) - fibromuscular dysplasia , medicine , renal artery stenosis , secondary hypertension , renal artery , stenosis , renovascular hypertension , angioplasty , renal artery obstruction , blood pressure , cardiology , angiography , percutaneous , radiology , dysplasia , kidney
Fibromuscular dysplasia is a rare noninflammatory vascular disease characterized by nonatheroslerotic stenosis predominantly seen in young women, whereas the majority of cases involve the renal arteries causing secondary hypertension. Most noninvasive screening tests are not quite sensitive or reproducible to rule out renal artery stenosis, but renal angiography usually confirms the diagnosis. Percutaneous renal artery angioplasty is the treatment of choice; however, it may not result in normalization of blood pressure if diagnosis is delayed. Continued follow‐up is necessary since stenosis reoccurs.