Premium
Temper outbursts in Lowe syndrome: Characteristics, sequence, environmental context and comparison to Prader–Willi syndrome
Author(s) -
Cressey Helen,
Oliver Chris,
Crawford Hayley,
Waite Jane
Publication year - 2019
Publication title -
journal of applied research in intellectual disabilities
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.056
H-Index - 63
eISSN - 1468-3148
pISSN - 1360-2322
DOI - 10.1111/jar.12613
Subject(s) - context (archaeology) , aggression , etiology , psychology , intellectual disability , sequence (biology) , developmental psychology , psychiatry , genetics , biology , paleontology
Background There is limited research into the nature and aetiology of temper outbursts in people with intellectual disabilities. In this study, we describe the phenomenology and environmental context of temper outbursts in Lowe syndrome, a rare genetic syndrome in which outbursts are purportedly frequent. Method A temper outburst interview (TOI) was conducted with caregivers of seventeen individuals with Lowe syndrome to generate an account of the behavioural sequence, common antecedents and consequences of temper outbursts, and to enable comparisons with similar work on Prader–Willi syndrome. Results Outbursts in Lowe syndrome were frequently triggered by thwarted goal‐directed behaviour and were associated with high levels of physical aggression and property destruction. Conclusions Form and sequence of outbursts showed similarities to Prader–Willi syndrome and to behaviours reported in literature on typically developing children. The results highlight the importance of considering shared aetiology as well as syndrome‐specific pathways in the development of outbursts.