Open AccessExtrathoracic malignant peripheral nerve sheath tumor of the lateral chest wall locally recurred and metastasized to peritoneum: Report of a case
Author(s) -
Gu Jundong,
Zhao Hui,
Xu Hongrui,
Zhu Siwei,
Li Li,
Yao Hong,
Wen Yanjun,
Wang Xinzhuo,
Wang Shuchuan,
Chen Jun,
Zhou Qinghua
Publication year - 2013
Publication title -
thoracic cancer
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.823
H-Index - 28
eISSN - 1759-7714
pISSN - 1759-7706
DOI - 10.1111/j.1759-7714.2012.00119.x
Subject(s) - medicine , peritoneum , peripheral , peripheral nerve , pathology , anatomy
Malignant peripheral nerve sheath tumors (MPNSTs) are rare, with an expected incidence of 0.0001% per year in the general population and 4.6% in patients with von Recklinghausen's disease. They are defined as any malignant tumors arising or differentiating from cells of the peripheral nerve sheath. MPNSTs can develop in various sites including the trunk and head/neck region. However, its onset on the chest wall is very rare. Here we report a case of MPNST growing outside the thorax on the chest wall. The patient developed a local recurrence twice, which caused multiple metastases to the lung and peritoneum.