Radius Maumenee Syndrome

Summary Ocular injection and increased IOP from elevated episcleral venous pressure are most frequently caused by carotid cavernous fistula. Other causes include large vessel venous obstruction (venous sinus thrombosis and superior vena cava syndrome), Sturge–Weber syndrome, scleritis, thyroid‐related orbitopathy and orbital tumours or orbital varices (Radius & Maumenee 1978; Rhee et al. 2009). Additionally, idiopathic rise in episcleral venous pressure, known as Radius–Maumenee syndrome, can lead to ocular injection with elevated IOP (Radius & Maumenee 1978). The syndrome was originally described by Minas & Podos (1968). The diagnosis is based on the clinical findings of elevated IOP causing glaucomatous optic nerve and visual field damage in association with an open angle and dilated episcleral veins. The diagnosis of Radius–Maumenee syndrome can only be made with confidence after intra‐orbital and intracranial pathology mentioned above has been excluded by MRI . Two case reports will illustrate the typical features of this rare cause of glaucoma.