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Congenital orbital teratoma
Author(s) -
ROSNER M,
FABIAN ID,
PRIEL A,
FRIDMAN E,
GREENBERG G,
ROSEN N
Publication year - 2012
Publication title -
acta ophthalmologica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.534
H-Index - 87
eISSN - 1755-3768
pISSN - 1755-375X
DOI - 10.1111/j.1755-3768.2012.3687.x
Subject(s) - medicine , teratoma , lesion , anatomy , pathology , radiology
Purpose Congenital orbital teratoma is a rare tumor, composed of all three germ cell layers. The purpose is to present a case with congenital orbital teratoma, and discuss the clinical and histological characteristics of the tumor. Methods Case report of a newborn girl that had a protrusion of the right globe. Imaging disclosed a big intraorbital lesion and capillary hemangioma was suspected, but treatment with propranolol had no effect during 4 months. At the age of 5 months acute progression of the proptosis developed with enlargement of the orbital mass as seen on MRI, pressing on the optic nerve. She underwent surgery and the lesion was removed completely using a cryo‐probe. Results The pathologic diagnosis was orbital teratoma including cysts filled with keratin, hair follicles, glands, bone, cartilage, epithelium and neuronal‐brain tissue. On follow‐up examination there was no proptosis but some limitation of ocular movements was seen one month after surgery. Conclusion In order to diagnose clinically orbital teratoma, a high index of suspicion is needed. Surgical excision is the treatment of choice. Early detection and treatment is important in order to prevent mechanical destruction of adjacent tissues.