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Best's macular dystrophy with a macular hole
Author(s) -
Mehta Mehul,
Katsumi Osamu,
Tetsuka Soichi,
Hirose Tatsuo,
Tolentino Felipe I.
Publication year - 1991
Publication title -
acta ophthalmologica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.534
H-Index - 87
eISSN - 1755-3768
pISSN - 1755-375X
DOI - 10.1111/j.1755-3768.1991.tb02010.x
Subject(s) - macular dystrophy , macular hole , medicine , ophthalmology , dystrophy , macula lutea , optometry , macular degeneration , retinal , visual acuity , pathology , vitrectomy
The occurrence of a macular hole with Best's dystrophy is an extremely rare finding with only one reported case in the literature. We wish to report two cases with typical Best's dystrophy in one eye and a macular hole in the contralateral eye. In one case the Pattern Reversal VER (PVER) was also recorded and graphed as an amplitude‐check size function curve. The PVER changes in this case were grossly subnormal in both the eyes, suggesting a significant degree of bilateral macular impairment. This implies that a significant amount of functional impairment occurs at the vitelliform stage itself, though how this stage progresses to a macular hole is unclear.