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ANTERIOR CHAMBER CLEAVAGE SYNDROME
Author(s) -
HOLMARK J.,
JENSEN O. A.
Publication year - 1972
Publication title -
acta ophthalmologica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.534
H-Index - 87
eISSN - 1755-3768
pISSN - 1755-375X
DOI - 10.1111/j.1755-3768.1972.tb06626.x
Subject(s) - sclera , cornea , anatomy , ophthalmology , medicine , descemet's membrane , aphakia , microphthalmia , intraocular pressure , biology , intraocular lens , biochemistry , gene
An otherwise healthy girl had from birth right‐sided microphthalmia with leukomatous cornea and left‐sided staphyloma centrally on a leu‐komatous cornea, surrounded by a deep blue sclera. The intraocular pressure was raised and the staphyloma increased in size. The eyeball was enucleated at three months of age and showed anterior chamber cleavage syndrome. The corneal stroma was replaced by connective tissue. No Bowman's membrane was found and the Descemet's membrane was present only as small coiled remnants centrally. No lens was observed. The iris was seen only in a few sections, as a string attached to the cornea. The posterior part of the eye was normal. The classification of the case is discussed and it is concluded that it can be considered an advanced atypical case of Peters' anomaly with the rarely seen primary aphakia and combined with Rieger's dysplasia.