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Oral findings and dental treatment in a child with West syndrome
Author(s) -
Regis Rômulo Rocha,
Rocha Cristiane Tomaz,
Torres Carolina Paes,
Queiroz Ivna Fernandes,
De Queiroz Alexandra Mussolino
Publication year - 2009
Publication title -
special care in dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.328
H-Index - 41
eISSN - 1754-4505
pISSN - 0275-1879
DOI - 10.1111/j.1754-4505.2009.00106.x
Subject(s) - medicine , hypsarrhythmia , oral hygiene , gingival enlargement , pediatrics , dental care , cusp (singularity) , dentistry , epilepsy , psychiatry , geometry , mathematics
West syndrome (WS) is a rare, severe form of epilepsy that typically manifests early in infancy. It is considered a malignant condition that combines episodes of spasms that occur in clusters (infantile spasm), hypsarrhythmia on the electroencephalogram, and neuropsychomotor delay. Although WS has been widely investigated from a medical standpoint, few reports have focused on the oral findings in patients with this syndrome. This article reports the case history of a 7‐year‐old child diagnosed with WS. The major clinical features were generalized tooth wear and gingival enlargement, altered chronology and sequence of dental eruption, primary canine cusp‐to‐cusp relationship, ectopic dental eruption, and mildly arched palate. Multiple white spot lesions were also observed, possibly associated with poor oral hygiene, due to a fermentable carbohydrate‐rich diet, and continuous use of sugar‐containing medications. Dental care management of patients with special needs is discussed and the dental treatment for this child with WS is described.