Premium
Pediatric dental management of a patient with osteogenesis imperfecta and dentinogenesis imperfecta
Author(s) -
Muhney Kelly,
Campbell Patricia Regener
Publication year - 2007
Publication title -
special care in dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.328
H-Index - 41
eISSN - 1754-4505
pISSN - 0275-1879
DOI - 10.1111/j.1754-4505.2007.tb01757.x
Subject(s) - dentinogenesis imperfecta , osteogenesis imperfecta , medicine , short stature , dentistry , connective tissue disorder , orthodontics , pediatrics , surgery , pathology
Osteogenesis imperfecta (OI) is a genetic disorder that affects all connective tissue. Clinical manifestations of OI include bone fragility, hyperlaxity of joints, hearing loss, abnormalities of stature and facial structure, blue scleras, and dentinogenesis imperfecta (DI). OI is classified into four groups according to the severity and physical characteristics of the disease, although not all characteristics may be present in one individual. Currently, 20,000 to 50,000 individuals in the U.S. have been diagnosed with this disease. The aim of this article is to discuss medical and dental complications associated with OI and DI. A case presentation describes the clinical cars of a patient from birth to age 12.