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Oral manifestations of Beckwith‐Wiedemann syndrome
Author(s) -
SALMAN RICHARD A.
Publication year - 1988
Publication title -
special care in dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.328
H-Index - 41
eISSN - 1754-4505
pISSN - 0275-1879
DOI - 10.1111/j.1754-4505.1988.tb00678.x
Subject(s) - macroglossia , medicine , beckwith–wiedemann syndrome , tongue , occlusion , pediatrics , intensive care medicine , surgery , pathology , biochemistry , gene expression , chemistry , dna methylation , gene
A report of case of a patient with Beckwith‐Wiedemann syndrome is presented. The macroglossia associated with the syndrome necessitated long‐term dental follow‐up to prevent and treat problems with occlusion, speech, and esthetic appearance that might develop. Early intervention might be required if feeding or respiratory difficulties, resulting from the macroglossia, arise. The diagnosis of the syndrome should alert the dentist to the increased incidence of intra‐abdominal malignancies and the need for periodic observation.