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Papillary fibroelastoma of the tricuspid valve presenting as neonatal pulmonary haemorrhage
Author(s) -
Sridhar AV,
Bulock F,
Hickey MStJ,
Chikermane A,
Black E,
Currie A
Publication year - 2004
Publication title -
acta pædiatrica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.772
H-Index - 115
eISSN - 1651-2227
pISSN - 0803-5253
DOI - 10.1111/j.1651-2227.2004.tb02759.x
Subject(s) - papillary fibroelastoma , medicine , tricuspid valve , presentation (obstetrics) , radiology , cardiac tumors , cardiology , surgery
Papillary fibroelastoma is a benign tumour of the cardiac valve apparatus. We present an unusual case of life‐threatening pulmonary haemorrhage and disseminated intravascular coagulation in a neonate associated with this benign cardiac tumour. Papillary fibroelastoma of the tricuspid valve rarely presents in children and, to our knowledge, this is only the second reported case in a neonate. The patient was successfully managed by anticoagulation therapy followed by surgical excision of the tumour. This case illustrates the potentially fatal presentation of this benign cardiac tumour among neonates. Conclusion : Pulmonary haemorrhage of this degree is unusual in an otherwise healthy term neonate and needs careful investigation for unusual pathology including potential sources of pulmonary emboli in the heart. We emphasize the value of echocardiography in the evaluation of unexpected pulmonary haemorrhage in the newborn.