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Recurrent Pseudomonas bronchopneumonia and other symptoms as in cystic fibrosis in a child with type I pseudohypoaldosteronism
Author(s) -
Marthinsen L,
Kornfält R,
Aili M,
Andersson D,
Westgren U,
Schaedel C
Publication year - 1998
Publication title -
acta pædiatrica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.772
H-Index - 115
eISSN - 1651-2227
pISSN - 0803-5253
DOI - 10.1111/j.1651-2227.1998.tb01483.x
Subject(s) - medicine , cystic fibrosis , pseudohypoaldosteronism , bronchopneumonia , pseudomonas aeruginosa , gastroenterology , pathological , urine , pathology , bacteria , aldosterone , biology , genetics
We report a child with multiple target organ pseudohypoaldosteronism type 1 with frequent recurrent pulmonary infections caused by Pseudomonas aeruginosa and Pasteurella multocida and high levels of chloride in sweat, urine and nasal secretion. Repetitive faecal chymotrypsin samples have all shown pathological values in spite of no other sign of exocrine pancreas dysfunction. The similarities with cystic fibrosis and the importance of the salt content in bronchial fluid are discussed.