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Intestinal pseudo‐obstruction syndrome in a child with myotonic dystrophy
Author(s) -
Bruinenberg JFM,
Rieu PNMA,
Gabreëls FM,
Tolboom J
Publication year - 1996
Publication title -
acta pædiatrica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.772
H-Index - 115
eISSN - 1651-2227
pISSN - 0803-5253
DOI - 10.1111/j.1651-2227.1996.tb13906.x
Subject(s) - medicine , myotonic dystrophy , intestinal pseudo obstruction , complication , myotonia , paralytic ileus , ileus , dystrophy , surgery , pediatrics , gastroenterology , pathology
Gastrointestinal symptoms in myotonic dystrophy are increasingly observed, but major intestinal movement disorders such as intestinal pseudo‐obstruction appear to be an infrequent complication. We describe a 13‐year‐old boy who, after appendectomy, developed intestinal pseudo‐obstruction syndrome as the first clinical manifestation of myotonic dystrophy. He developed several similar episodes thereafter, which responded to conservative measures. When a child with myotonic dystrophy presents with an ileus, the diagnosis of intestinal pseudo‐obstruction should be considered and therapy should then be conservative.