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Agenesis of pancreas
Author(s) -
Voldsgaard P,
KrygerBaggesen N,
Lisse I
Publication year - 1994
Publication title -
acta pædiatrica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.772
H-Index - 115
eISSN - 1651-2227
pISSN - 0803-5253
DOI - 10.1111/j.1651-2227.1994.tb13144.x
Subject(s) - medicine , agenesis , meconium ileus , meconium , pancreas , pathogenesis , metabolic acidosis , surgery , pregnancy , fetus , biology , genetics
Complete agenesis of pancreas is a rare and lethal condition. Four cases have previously been reported in combination with other malformations, such as severe intrauterine growth retardation, hyperglycaemia and meconium ileus. We report a case of pancreatic agenesis as a single anomaly. The child died when 48 h old with severe metabolic acidosis. The literature is surveyed and the pathogenesis is discussed.