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Non‐immune hydrops fetalis and bilateral pulmonary hypoplasia in a newborn infant with extralobar pulmonary sequestration
Author(s) -
Brus F,
Nikkels PGJ,
Loon AJ van,
Okken A
Publication year - 1993
Publication title -
acta pædiatrica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.772
H-Index - 115
eISSN - 1651-2227
pISSN - 0803-5253
DOI - 10.1111/j.1651-2227.1993.tb12710.x
Subject(s) - medicine , hydrops fetalis , polyhydramnios , pulmonary sequestration , pulmonary hypoplasia , hydrothorax , chylothorax , hypoplasia , lung , fetus , surgery , pregnancy , ascites , genetics , biology
Extralobar pulmonary sequestration was found in a newborn premature infait that presented with non‐immune hydrops fetalis, massive bilateral hydrothorax and polyhydramnios in utero. The baby died of severe respiratory insufficiency 15 h after birth. Postmortem examination revealed distended lymphatic vessels in the sequestered lung tissue probably due to impeded lymph drainage. We suggest that not extralobar pulmonary sequestration itself but a subsequent massive unilateral hydrothorax due to severe obstruction of lymph drainage was the cause of the non‐immune hydrops fetalis, pulmonary hypoplasia and polyhydramnios. If these symptoms are diagnosed before delivery, a search for extralobar pulmonary sequestration is indicated.