Premium
Klippel–Trenaunay syndrome
Author(s) -
Auluck A,
Suhas S,
Pai KM
Publication year - 2005
Publication title -
oral diseases
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.953
H-Index - 87
eISSN - 1601-0825
pISSN - 1354-523X
DOI - 10.1111/j.1601-0825.2005.01072.x
Subject(s) - klippel trenaunay syndrome , craniofacial , medicine , venous malformation , oral cavity , craniofacial abnormality , congenital disorder , soft tissue , vascular malformation , pathology , anatomy , dermatology , radiology , dentistry , psychiatry
Klippel–Trenaunay syndrome (KTS) is a congenital disorder characterized by triad of vascular nevi, venous varicosities and hyperplasia of soft and hard tissues in the affected area. This syndrome usually affects the extremities but occasionally can manifest in the craniofacial region, including the oral cavity. We report a case of KTS and discuss the oro‐surgical and dental considerations regarding hemorrhagic tendencies caused by the known local anomalies such as vascular malformations associated with this syndrome as well as systemic abnormalities.