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Odontogenic myxoma in an adolescent with tuberous sclerosis
Author(s) -
Harrison M. G.,
O'Neill I. D.,
Chadwick B. L.
Publication year - 1997
Publication title -
journal of oral pathology and medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.887
H-Index - 83
eISSN - 1600-0714
pISSN - 0904-2512
DOI - 10.1111/j.1600-0714.1997.tb00226.x
Subject(s) - tuberous sclerosis , medicine , odontogenic myxoma , enamel hypoplasia , pathology , amelogenesis imperfecta , odontogenic , dermatology , enamel paint , dentistry
Tuberous sclerosis is a hamarloneoplastic syndrome characterised by early onset of convulsive seizures with mental retardation. Oral abnormalities, including enamel hypoplasia and mucosal fibromas, have been previously reported. We report here a 17‐year‐old girl with this disorder who had received repeated dental trauma. She presented with a swelling associated with a traumatised maxillary central incisor that suggested a diagnosis other than the Odontogenic myxoma found at operation. Odontogenic myxoma has not previously been reported in this condition; it may represent an unusual phenotypic expression of the genetic defect understood to determine tuberous sclerosis, or it may be an unrelated coincidental finding.