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Hereditary gingival fibromatosis in a family with the Zimmermann Laband syndrome
Author(s) -
Bakaeen Ghazi,
Scully Crispian
Publication year - 1991
Publication title -
journal of oral pathology and medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.887
H-Index - 83
eISSN - 1600-0714
pISSN - 0904-2512
DOI - 10.1111/j.1600-0714.1991.tb00438.x
Subject(s) - hypertrichosis , medicine , fibromatosis , dermatology , cowden syndrome , gingivectomy , alopecia areata , pathology , biology , dentistry , germline mutation , mutation , genetics , gene
Hereditary gingival fibromatosis is frequently an isolated condition of little consequence apart from a cosmetic problem and occasional associations with hypertrichosis and/or epilepsy. There are, however, several uncommon or rare eponymous syndromes described in which gingival fibromatosis can be a feature: these include the Zimmermann‐Laband, Murray‐Puretic‐Drescher, Rutherfurd, Cowden and Cross syndromes. This paper describes two siblings with features of the rare Zimmermann‐Laband syndrome and discusses the major aspects of this and other eponymous syndromes that may be associated with hereditary gingival fibromatosis.