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Epstein syndrome: oral lesions in a patient with nephropathy, deafness and thrombocytopenia
Author(s) -
Richards A.,
Scully C.,
Eveson J.,
Prime S.
Publication year - 1991
Publication title -
journal of oral pathology and medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.887
H-Index - 83
eISSN - 1600-0714
pISSN - 0904-2512
DOI - 10.1111/j.1600-0714.1991.tb00415.x
Subject(s) - medicine , nephropathy , dermatology , nephritis , pathology , pediatrics , diabetes mellitus , endocrinology
Epstein syndrome is a rare dominantly inherited disorder in which the main features are nephritis, deafness and macrothrombocytopathic thrombocytopenia. A case with oral haemorrhage and purpuric lesions is reported. This appears to be the first report of this syndrome in the dental literature.