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Adult Langerhans cell histiocytosis
Author(s) -
Stockschlaeder Marcus,
Sucker Christoph
Publication year - 2006
Publication title -
european journal of haematology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.904
H-Index - 84
eISSN - 1600-0609
pISSN - 0902-4441
DOI - 10.1111/j.1600-0609.2006.00648.x
Subject(s) - langerhans cell histiocytosis , histiocyte , histiocytosis , presentation (obstetrics) , medicine , disease , pathology , multisystem disease , histiocytosis x , dermatology , radiology
Langerhans cell histiocytosis (LCH) is a proliferative histiocytic disorder of unknown cause originating from dendritic cells. The clinical presentation of LCH is highly variable. Although the features of this disease have been well described in children, they remain poorly defined in adults. Here, we review the current knowledge about adult LCH, focussing on clinical presentation, diagnosis, treatment, and prognosis.