Premium
Cardiac Surgery in Patients with Acute Intermittent Porphyria
Author(s) -
Benassi Filippo,
Righi Elena,
Cimato Paolo,
Parravicini Roberto
Publication year - 2012
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/j.1540-8191.2011.01350.x
Subject(s) - medicine , acute intermittent porphyria , perioperative , porphyria , endocarditis , cardiac surgery , infective endocarditis , intensive care medicine , surgery
A bstract Acute intermittent porphyria (AIP) is a disorder of the heme biosynthesis pathway of a specific inherited enzymatic defect. Many different environmental factors such as drugs, calorie restriction, infection etc., often play a key role in triggering a porphiric acute attack. We describe a 50‐year‐old woman with AIP who underwent aortic valve replacement due to acute infective endocarditis and review the perioperative management of these patients. (J Card Surg 2012;27:331–334)