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Total Aortic Replacement in Loeys‐Dietz Syndrome
Author(s) -
Williams Judson B.,
McCann Richard L.,
Hughes G. Chad
Publication year - 2011
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/j.1540-8191.2011.01224.x
Subject(s) - medicine , aortic root , aortic valve replacement , aortic arch , surgery , cardiology , aorta , stenosis
Abstract Loeys‐Dietz syndrome (LDS) is a recently identified genetic complex characterized in part by rapidly progressive aortic and branch vessel disease. We now describe total aortic replacement using an open Extent II thoracoabdominal repair followed by second‐stage redo‐sternotomy for a valve‐sparing aortic root replacement and hybrid aortic arch repair in a patient with this syndrome. (J Card Surg 2011;26:304‐308)