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Primary Malignant Fibrous Histiocytoma of the Heart with Skeletal Muscles Metastases
Author(s) -
Milicic Davor,
Juretic Antonio,
Bulum Josko,
Saric Nera,
Bisof Vesna,
Jelic Ivan,
Jelasic Drazen
Publication year - 2007
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/j.1540-8191.2007.00451.x
Subject(s) - medicine , primary (astronomy) , heart neoplasms , pathology , physics , astronomy
Malignant fibrous histiocytoma is an extremely rare primary malignant tumor of the heart. It is usually diagnosed when it is locally aggressive or has already metastasized. The prognosis is poor with an average survival time of one year. We report a case of recurrent left atrial malignant fibrous histiocytoma initially misdiagnosed as myxoma. The patient underwent repeated surgical resections followed by chemotherapy. Despite adjuvant chemotherapy, 18 months after initial diagnosis, definitive tumor relapse in left atrium was diagnosed. This is the 48th case of primary cardiac fibrous malignant histiocytoma reported in the literature.