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Combined Valve and Coronary Surgery in a Patient with Erythropoietic Protoporphyria
Author(s) -
Akıncı Esat,
Erentug Vedat,
Bozbuga Nilgun,
Polat Adil,
Mansuroglu Denyan,
Yakut Cevat
Publication year - 2005
Publication title -
journal of cardiac surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.428
H-Index - 58
eISSN - 1540-8191
pISSN - 0886-0440
DOI - 10.1111/j.1540-8191.2005.200438.x
Subject(s) - medicine , erythropoietic protoporphyria , surgery , cardiology , protoporphyrin , chemistry , porphyrin , photochemistry
Erythropoietic protoporphyria (EPP) is an autosomal dominant disorder of heme synthesis, causing excess of protoporphyrin in blood, skin, liver, and other organs. A 58‐year‐old male patient with EPP underwent aortic valve replacement and a concomitant aortocoronary bypass. The patient has been followed without complications due to EPP postoperatively. Cardiac surgery can safely be performed on patients with EPP by considering close attention not to stimulate porphyrin synthesis.