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Isolated Noncompaction of Right Ventricle—A Case Report
Author(s) -
Ranganathan Arun,
Ganesan Gnanavelu,
Sangareddi Venkatesan,
Pillai Arunachalam Piramanayagam,
Ramasamy Alagesan
Publication year - 2012
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/j.1540-8175.2012.01671.x
Subject(s) - ventricle , cardiology , medicine , heart failure , left ventricular noncompaction , magnetic resonance imaging , cardiomyopathy , cardiac magnetic resonance , right heart failure , atrial fibrillation , cardiac magnetic resonance imaging , radiology
Isolated noncompaction of ventricular myocardium (INVM) is a genetic cardiomyopathy due to abnormal arrest in endomyocardial embryogenesis between fetal 5th and 8th week. Noncompaction of right ventricle alone is rare. Here we present one such case where a young man presented with progressive right heart failure and atrial fibrillation. Subsequent evaluation by echo and cardiac magnetic resonance imaging confirmed our diagnosis. The cardinal manifestations of INVM are heart failure, arrhythmia, and embolic events and our case presented with former two manifestations. Echocardiographic criteria for diagnosing INVM are discussed.