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An Unusual Case of Congenitally Corrected Transposition of the Great Arteries Associated with Noncompaction‐Like Remodeling of the Morphological Right Ventricle
Author(s) -
Kharge Jayashree,
Prasad Murigendrappa Renuka,
Ramegowda Raghu Thagachagere
Publication year - 2011
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/j.1540-8175.2011.01485.x
Subject(s) - great arteries , medicine , ventricle , cardiology , atrioventricular valve , regurgitation (circulation) , corrected transposition , anatomy
Congenitally corrected transposition of the great arteries is a rare disease characterized by atrio‐ventricular and ventriculo‐arterial discordance (double discordance) and is associated with other cardiac anomalies in the majority of cases. The important associated anomalies include ventricular septal defect, abnormalities of left atrioventricular valve, subpulmonary stenosis, and conduction abnormalities. However, the noncompaction‐like remodeling of the subaortic, morphologic right ventricle is not a commonly reported association. We, report a case of congenitally corrected transposition of the great arteries in a 40‐year‐old male patient, who had noncompaction‐like remodeling of the morphologic right ventricle with severe ventricular dysfunction. He also had, left‐sided Ebstein's anomaly, severe left atrioventricular valve regurgitation and a 2:1 atrioventricular conduction block. (Echocardiography 2011;28:E212‐E214)