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Isolated Congenital Left‐Sided Pulmonary Vein Stenosis in an Adult Patient Misdiagnosed as Primary Pulmonary Hypertension
Author(s) -
Kapoor Aditya,
Walia Rohit,
Jain Sunil K.,
Kumar Sudeep,
Radhakrishnan S.
Publication year - 2011
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/j.1540-8175.2010.01345.x
Subject(s) - medicine , pulmonary vein stenosis , pulmonary hypertension , heart disease , cardiology , stenosis , pulmonary vein , left pulmonary vein , surgery , radiology , ablation
Pulmonary vein stenosis (PVS) is a rare condition, seen usually in association with congenital heart disease or secondary to various acquired causes. Isolated PVS, in adults, especially in absence of congenital heart disease is extremely uncommon. We report PVS of left sided pulmonary veins in an 18‐year‐old male, who had been till then diagnosed as primary pulmonary hypertension (PPH). (Echocardiography 2011;28:E97‐E100)