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Early Prenatal Echocardiographic Diagnosis of Cantrell Pentology with Hypoplastic Right Heart Syndrome
Author(s) -
SELIEM MOHAMED A.,
MANASRA KHADER,
MIGUEL RICHARD SAN,
PALILEO MAE R.
Publication year - 1995
Publication title -
echocardiography
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.404
H-Index - 62
eISSN - 1540-8175
pISSN - 0742-2822
DOI - 10.1111/j.1540-8175.1995.tb00565.x
Subject(s) - medicine , hypoplastic left heart syndrome , diaphragm (acoustics) , fetus , prenatal diagnosis , diaphragmatic breathing , fetal echocardiography , gestation , anatomy , cardiology , abdominal wall , pregnancy , heart disease , pathology , physics , alternative medicine , biology , acoustics , loudspeaker , genetics
Pentology of Cantrell is a complex syndrome involving the thoracic and abdominal walls, the diaphragm, and the heart. We report a case of that syndrome diagnosed early in pregnancy (16 weeks gestation) by fetal echocardiogram. The fetus had a severe form of hypoplastic right heart syndrome. Early diagnosis of such complex cardiac anatomy together with other severe anatomical malformations is important in planning the surgical intervention. It also shows the intimate relationship between the developmental anatomy and physiology of the fetal heart.