Premium
Pathologic Findings Following Sudden Death in an Infant with Hypertrophic Cardiomyopathy and Supraventricular Tachycardia
Author(s) -
KANTER RONALD J.,
GRAVATT ANDREA,
BHARATI SAROJA
Publication year - 1997
Publication title -
journal of cardiovascular electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.193
H-Index - 138
eISSN - 1540-8167
pISSN - 1045-3873
DOI - 10.1111/j.1540-8167.1997.tb00783.x
Subject(s) - medicine , hypertrophic cardiomyopathy , supraventricular tachycardia , cardiology , sudden death , cardiomyopathy , tachycardia , supraventricular arrhythmia , atrial fibrillation , heart failure
Sudden Infant Death in Hypertrophic Cardiomyopathy. The cardiac conduction system from infants suddenly dying with hypertrophic cardiomyopathy has not been described. We studied by serial section examination the conduction system from a 13‐month old infant also known to have had supraventricular tachycardia. At autopsy, there was cardiomegaly with asymmetric septal hypertrophy. Microscopic examination revealed myofiber disarray around an abnormally formed central fibrous body, numerous nodoventricular fibers to both sides of the ventricular septum, and fibrosis of the left bundle branch. We postulate that supraventricular tachycardia utilized a concealed pathway or the malformed AV Junction. Death may have resulted from deranged hemodynamics secondary to supraventricular tachycardia.