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Fetal and Neonatal Presentation of Long QT Syndrome
Author(s) -
KOMARLU RUKMINI,
BEERMAN LEE,
FREEMAN DAVID,
ARORA GAURAV
Publication year - 2012
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/j.1540-8159.2011.03040.x
Subject(s) - medicine , long qt syndrome , torsades de pointes , hydrops fetalis , in utero , presentation (obstetrics) , fetus , tachycardia , pediatrics , qt interval , cardiology , obstetrics , pregnancy , biology , genetics
This report describes a fetus presenting with intrauterine tachycardia and hydrops fetalis. Soon after birth the neonate was noted to be in torsades de pointes that responded dramatically to medical management. Long QT syndrome (LQTS) was diagnosed on electrocardiogram obtained soon after birth. The prognosis is poor when LQTS presents in utero or during the first week of life. However, our infant did well with medical management and has remained free of arrhythmias at follow‐up. PACE 2012; 35:e87–e90)