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A Young Patient with Danon Disease Receives Two ICD Shocks: Why?
Author(s) -
ZANNAD NOURA,
PIERRE BERTRAND,
COSNAY PIERRE,
BABUTY DOMINIQUE
Publication year - 2010
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/j.1540-8159.2010.02696.x
Subject(s) - medicine , cardiology , disease , intensive care medicine
We report the case of an 18‐year‐old man with Danon disease, a genetic disorder inclunding a severe hypertrophic cardiomyopathy with very broad QRS, who had an implantable cardioverter defibrillator for primary prevention. Nine months after implantation, he received two inappropriate shocks due to R‐wave double counting during sinus tachycardia. We discuss how to avoid such inappropriate therapy. (PACE 2010; 618–619)