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Pharmacological Treatment of Electrical Storm in Cathecolaminergic Polymorphic Ventricular Tachycardia
Author(s) -
FAGUNDES ALEXSANDRO,
DE MAGALHAES LUIZ PEREIRA,
RUSSO MARCELO,
XAVIER EDVALDO
Publication year - 2010
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/j.1540-8159.2009.02586.x
Subject(s) - medicine , ventricular tachycardia , cardiology , implantable cardioverter defibrillator , catecholaminergic polymorphic ventricular tachycardia , storm , refractory (planetary science) , tachycardia , ryanodine receptor 2 , physics , oceanography , ryanodine receptor , astrobiology , calcium , geology
We present a case of a young boy who had an implantable cadrioverter defibrillator implanted for refractory syncope and cathecolaminergic polymorphic ventricular tachycardia (CPVT). The patient underwent an electrical storm with multiple shocks and serious compromise of quality of life and risk. The pharmacological options are discussed as well as the strategies of managing ventricular arrhythmias in CPVT. (PACE 2010; 33:e27–e31)