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Rhythm Abnormalities in Children with Isolated Ventricular Noncompaction
Author(s) -
ÇELIKER ALPAY,
ÖZKUTLU SÜHEYLA,
DILBER EMBIYA,
KARAGÖZ TEVFIK
Publication year - 2005
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/j.1540-8159.2005.09498.x
Subject(s) - medicine , cardiology , left ventricular noncompaction , ventricular tachycardia , cardiomyopathy , sinus rhythm , heart failure , implantable cardioverter defibrillator , bradycardia , heart rate , atrial fibrillation , blood pressure
Background: Isolated ventricular noncompaction (IVNC) is a serious cardiomyopathy with a generally poor prognosis. It is characterized by the presence of prominent ventricular myocardial trabeculations and deep intertrabecular recesses, in the absence of other structural heart defects. This cardiomyopathy is usually associated with ventricular dysfunction, thromboembolic events, and rhythm problems.Methods and Results: This article describes 11 children who have rhythm abnormalities associated with IVNC. On admission, eight children had complaints including palpitation, syncope, heart failure, and bradycardia. Ventricular arrhythmias were diagnosed in four children, sinus node and atrioventricular conductance disturbances in six children, and Wolff‐Parkinson‐White syndrome and associated tachycardia in one child. Three children with ventricular arrhythmias received an automatic implantable cardioverter defibrillator (ICD). Three patients died of cardiac problems during the follow‐up period.Conclusion: Since many of rhythm abnormalities, including life‐threatening ventricular arrhythmias, may be seen in patients with IVNC, children with IVNC should be screened for arrhythmias. An ICD may be the best treatment for some of these patients.