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Ventricular Tachycardias and Dilated Cardiomyopathy Caused by Fabry Disease
Author(s) -
IGAWA OSAMU,
MIAKE JUNICHIRO,
HISATOME ICHIRO
Publication year - 2005
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/j.1540-8159.2005.00241.x
Subject(s) - medicine , amiodarone , cardiology , fabry disease , dilated cardiomyopathy , cardiomyopathy , ventricular tachycardia , disease , implantable cardioverter defibrillator , heart disease , atrial fibrillation , heart failure
Women with Fabry disease are considered to have a good prognosis. Here we report the clinical history of a female patient with severe Fabry disease before and after referral to our hospital. She was diagnosed to have a cardiac variant of Fabry disease since a left ventricular endmyocardial biopsy revealed specific features of this disease and that cardiac involvement was the sole manifestation. She developed sustained ventricular tachycardia and dilated cardiomyopathy requiring oral administration of amiodarone and a cardiac defibrillator implant.