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Hypersensitive Carotid Sinus Syndrome Due to Neurofibromatosis‐1 and Manifested by Repeated Episodes of Syncope
Author(s) -
SUTHERLAND JESSICA A.,
STOBIE PAUL,
SWARUP VIJAY,
TIERNEY SEAN P.,
LIN ALBERT C.,
BURKE MARTIN C.
Publication year - 2004
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/j.1540-8159.2004.00680.x
Subject(s) - medicine , syncope (phonology) , asystole , neurofibromatosis , neck mass , carotid sinus , cardiology , sinus (botany) , surgery , anesthesia , radiology , botany , biology , genus , reflex
A 28‐year‐old patient with neurofibromatosis‐1 presented with syncope. The exam demonstrated a mass adjacent and inferior to the right occiput that extended to the posterior lateral right‐sided neck. Initial invasive and noninvasive testing was negative. Imaging of her head and neck demonstrated a large neurofibroma enveloping her right carotid sinus without vessel occlusion or evidence of malignancy. An event recorder documented asystole. A pacemaker was implanted to avoid the surgical morbidity of removing the neck mass. The patient has since been free of syncope. We believe neurofibromatosis‐1 should be included in the differential of syncope.