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Implantable Defibrillator Therapy in Naxos Disease
Author(s) -
GATZOULIS KOSTAS,
PROTONOTARIOS NIKOS,
ANASTASAKIS ARIS,
TSATSOPOULOU ADALENA,
VLASSEROS JOHN,
GIALAFOS JOHN,
TOUTOUZAS PAVLOS
Publication year - 2000
Publication title -
pacing and clinical electrophysiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.686
H-Index - 101
eISSN - 1540-8159
pISSN - 0147-8389
DOI - 10.1111/j.1540-8159.2000.tb00922.x
Subject(s) - medicine , life expectancy , cardiology , disease , cardiomyopathy , sudden cardiac death , implantable cardioverter defibrillator , sudden death , heart disease , intensive care medicine , heart failure , population , environmental health
Naxos disease is a unique form of right ventricular cardiomyopathy with a high prevalence of malignant ventricular arrhythmias, including sudden cardiac death. As a hereditary systemic disease confined to a small island, it has been closely studied over the last 15 years. The implantation of an automatic defibrillator provides an alternative form of antiarrhythmic management to improve life expectancy in these high risk cardiac patients. We present the first two Naxos disease patients with malignant ventricular arrhythmias who had defibrillator implantation.