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Eyelid myoclonia with absences (Jeavons syndrome): A well‐defined idiopathic generalized epilepsy syndrome or a spectrum of photosensitive conditions?
Author(s) -
Striano Salvatore,
Capovilla Giuseppe,
Sofia Vito,
Romeo Antonino,
Rubboli Guido,
Striano Pasquale,
Trenité Dorothée KasteleijnNolst
Publication year - 2009
Publication title -
epilepsia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.687
H-Index - 191
eISSN - 1528-1167
pISSN - 0013-9580
DOI - 10.1111/j.1528-1167.2009.02114.x
Subject(s) - epilepsy , eyelid , myoclonus , idiopathic generalized epilepsy , electroencephalography , dermatology , pediatrics , myoclonic jerk , medicine , neurological disorder , generalized epilepsy , epilepsy syndromes , psychology , anesthesia , central nervous system disease , surgery , psychiatry
Summary Eyelid myoclonia with absences (EMA), or Jeavons syndrome, is a generalized epileptic condition clinically characterized by eyelid myoclonia (EM) with or without absences, eye closure‐induced electroencephalography (EEG) paroxysms, and photosensitivity; in addition, rare tonic–clonic seizures may also occur. Although first described in 1977 and widely reported by several authors within the last few years, EMA has not been yet recognized as a definite epileptic syndrome. However, when strict criteria are applied to the diagnosis, EMA appears to be a distinctive condition that could be considered a myoclonic epileptic syndrome, with myoclonia limited to the eyelids, rather than an epileptic syndrome with absences.