Premium
Epilepsy in the Setting of Neurocutaneous Syndromes
Author(s) -
Kotagal Prakash,
Rothner A. David
Publication year - 1993
Publication title -
epilepsia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.687
H-Index - 191
eISSN - 1528-1167
pISSN - 0013-9580
DOI - 10.1111/j.1528-1167.1993.tb06261.x
Subject(s) - tuberous sclerosis , epilepsy , neurofibromatosis , medicine , neurofibromatoses , genetic syndromes , dermatology , epilepsy syndromes , pediatrics , pathology , psychiatry
The neurocutaneous syndromes are characterized by congenital dysplastic abnormalities involving the skin and nervous system. The commonest neurocutaneous syndromes manifesting epilepsy are tuberous sclerosis and the Sturge‐Weber syndrome. Neurofibromatosis and other lesser‐known entities, such as epidermal nevus syndrome, are also known to be accompanied by epilepsy. These syndromes are not related to one another. This article reviews what has been learned about the epileptic syndromes in these disorders.