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“Obtundation Status (Dravet)” Caused by Complex Partial Status Epilepticus in a Patient with Severe Myoclonic Epilepsy in Infancy
Author(s) -
Wakai Shuji,
Ikehata Masami,
Nihira Hiroshi,
Ito Nozomi,
Sueoka Hirofumi,
Kawamoto Yoshitaka,
Hayasaka Hiroyuki,
Chiba Shunzo
Publication year - 1996
Publication title -
epilepsia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.687
H-Index - 191
eISSN - 1528-1167
pISSN - 0013-9580
DOI - 10.1111/j.1528-1157.1996.tb00542.x
Subject(s) - dravet syndrome , status epilepticus , ictal , myoclonic epilepsy , epilepsy , electroencephalography , anesthesia , pediatrics , medicine , psychology , myoclonic jerk , myoclonus , psychiatry
Summary:Purpose : We report a 1‐year 7‐month‐old boy with severe myoclonic epilepsy in infancy (SME) who exhibited complex partial status epilepticus (CPSE), which was confirmed by ictal video‐EEG analysis. This boy first had a hemi‐convulsion in a hot bath at age 3 months. Thereafter, he exhibited both partial and generalized seizures that were extremely intractable. At age 9 months, he had a prolonged episode of impaired consciousness that fit the “obtundation status in SME” defined by Dravet et al. Methods and Results : Ictal EEG revealed persisting irregular spike‐and‐wave complexes over the left hemisphere, predominantly in the occipitotemporal area, and confirmed CPSE. The EEG abnormalities with decreased level of the consciousness continued ‐6 h after onset of the symptoms even with AED administration. Conclusions : Because SME features both generalized and focal seizures, both types of nonconvulsive status may be seen in SME. Although Dravet et al. already reported long‐lasting atypical absences in patients with SME as “obtundation status,” we demonstrated CPSE in an infant with SME who exhibited a prolonged stuporous state.