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Spontaneous Intracranial Hypotension Syndrome in a Patient With Marfan Syndrome and Autosomal Dominant Polycystic Kidney Disease
Author(s) -
Albayram Sait,
Baş Ahmet,
Ozer Harun,
Dikici Suleyman,
Gulertan Serap Yavuz,
Yuksel Adnan
Publication year - 2008
Publication title -
headache: the journal of head and face pain
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.14
H-Index - 119
eISSN - 1526-4610
pISSN - 0017-8748
DOI - 10.1111/j.1526-4610.2007.01033.x
Subject(s) - medicine , epidural blood patch , autosomal dominant polycystic kidney disease , marfan syndrome , connective tissue disorder , cerebrospinal fluid , polycystic kidney disease , connective tissue , orthostatic vital signs , intracranial hypotension , connective tissue disease , weakness , surgery , anesthesia , disease , pathology , blood pressure , autoimmune disease
Intracranial hypotension is typically manifested by orthostatic headache. The most frequent underlying factor is cerebrospinal fluid leakage. It has been suggested that dural structural weakness in some connective tissue diseases may be responsible for dural tears and diverticula and consequently leakage. We present a case of spontaneous intracranial hypotension associated with Marfan syndrome and autosomal dominant polycystic kidney disease. The patient was treated successfully with epidural autologous blood patch. Dural involvements of these hereditary connective tissue diseases are also discussed.