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Type V Aplasia Cutis Congenita: Case Report, Review of the Literature, and Proposed Treatment Algorithm
Author(s) -
Morrow Daniel,
Schelonka Robert,
Krol Alfons,
Davies Michael,
Kuang Anna
Publication year - 2012
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2012.01742.x
Subject(s) - aplasia cutis congenita , medicine , trunk , conservative management , algorithm , surgery , dermatology , scalp , ecology , computer science , biology
Aplasia cutis congenita (ACC) is the congenital absence of skin. There are a number of different classifications based on distribution and associated findings. Type V ACC is unique in that the lesions are typically symmetric and found primarily on the trunk but can also include the upper and lower extremities. Type V is associated with the loss of a monozygotic co‐twin during the late first or early second trimester. Here we present an extensive case of type V ACC and a review of the literature, including a summary of treatment and outcomes. From the available literature, it appears that there is no benefit from early surgical intervention, and therefore we propose a treatment algorithm that starts with conservative management.