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Linear Immunoglobulin A Bullous Disease of Childhood Responsive to Intravenous Immunoglobulin Monotherapy
Author(s) -
Nanda Arti,
Khawaja Fatima,
Nanda Mousmee,
AlSabah Humoud,
Selim Mohamed K.,
Dvorak Richard,
Alsaleh Qasem A.
Publication year - 2011
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2011.01475.x
Subject(s) - dapsone , medicine , antibody , immunoglobulin g , intravenous immunoglobulin therapy , immunoglobulin a , disease , immunology , gastroenterology
We report a case of linear immunoglobulin A bullous disease in a 9‐year‐old boy who presented with rapidly progressive severe disease and could not tolerate dapsone because of high liver enzymes within a week after a low dose of dapsone in association with an underlying fatty liver. He showed remarkable improvement with intravenous immunoglobulins used as monotherapy, with a rapid clearance and a sustained remission after stopping the treatment.