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Is Langerhan Cell Histiocytosis Complicated with Hydrops Fetalis Exclusively Lethal in Premature Neonates?
Author(s) -
CHENG I,
CHEN YILIN,
TSAI YULUAN,
CHOU YUHYU,
SUNG TSENGCHEN,
MU SHUCHI
Publication year - 2011
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2011.01310.x
Subject(s) - medicine , hydrops fetalis , respiratory distress , langerhans cell histiocytosis , pleural effusion , histiocytosis , fetus , pathology , disease , pregnancy , surgery , genetics , biology
Langerhans cell histiocytosis is a rare disease and is lethal in premature neonates. A male premature neonate born at gestational 33 weeks presented with generalized vesicles, hydrops fetalis with pleural effusion, bilateral cataracts, and severe respiratory distress syndrome complicated with persistent pulmonary hypertension. Skin biopsy confirmed the diagnosis of Langerhans cell histiocytosis.