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Malignant Atrophic Papulosis: A Case Report with Severe Visual and Neurological Impairment
Author(s) -
GutiérrezPascual Marta,
HernándezMartín Angela,
Colmenero Isabel,
GarcíaPeñas Juan José,
LópezPino Miguel Angel,
Torrelo Antonio
Publication year - 2010
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2010.01287.x
Subject(s) - medicine , dermatology , gastrointestinal tract , disease , pathology
Abstract: Malignant atrophic papulosis, or Degos’ disease, is a severe systemic vasculopathy extremely rare in children. The skin, gastrointestinal tract, and central nervous system are most frequently affected. We report a 5‐year‐old girl with malignant atrophic papulosis who presented with widespread skin lesions from early infancy and severe visual and neurological impairment.