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Porokeratotic Eccrine Duct and Hair Follicle Nevus (PEHFN) Associated with Keratitis‐Ichthyosis‐Deafness (KID) Syndrome
Author(s) -
Criscione Vincent,
Lachiewicz Anne,
RobinsonBostom Leslie,
Grenier Nicole,
Dill Sara Worthing
Publication year - 2010
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2010.01272.x
Subject(s) - medicine , dermatology , hair follicle , ichthyosis , nevus , anatomy , pathology , melanoma , cancer research
Porokeratotic eccrine ostial and dermal duct nevus is a rare hamartomatous malformation, histologically characterized by cornoid lamellae overlying dilated eccrine ostia. The nevus most commonly presents in the form of multiple filiform keratotic spines in a linear arrangement, usually on the distal extremities (1). Porokeratotic eccrine and hair follicle nevus is thought to be a variant of porokeratotic eccrine ostial and dermal duct nevus that additionally involves hair follicle infundibula. We report a case of widespread Porokeratotic eccrine and hair follicle nevus that developed in a 15‐year‐old woman with keratitis‐ichthyosis‐deafness syndrome.