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Ligneous Conjunctivitis with Oral Mucous Membrane Involvement and Decreased Plasminogen Level
Author(s) -
ElDarouti Mohamed,
Zayed Amira A.,
ElKamah Ghada Y.,
Mostafa Mostafa I.
Publication year - 2009
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2009.00951.x
Subject(s) - medicine , dermatology , mucous membrane , pathology , gastroenterology
Ligneous conjunctivitis (MIM 217090) is a rare autosomal recessive hereditary disorder. We report a case with both ligneous conjunctivitis and ligneous periodontitis in association with plasminogen type I deficiency. Diagnosis was based on the clinical and histological findings and most importantly, decreased serum level of plasminogen type I.