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An Unusual Case of Congenital Linear Eccrine Spiradenoma
Author(s) -
RodríguezMartín Marina,
Sánchez González Rosalba,
SáezRodríguez Miguel,
GarcíaBustínduy M.,
MartínHerrera Antonio,
NodaCabrera Antonio
Publication year - 2009
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2009.00879.x
Subject(s) - medicine , asymptomatic , presentation (obstetrics) , trunk , nodule (geology) , dermatology , radiology , pathology , ecology , paleontology , biology
Eccrine spiradenoma (ES) is a benign uncommon tumor of skin adnexa with a characteristic clinical and histopathological presentation. Typically, it presents as a painful, slow growing and solitary nodule on the head or upper trunk in adult patients. We report a child with linear ES which presented with asymptomatic papulonodular lesions in a blaschkoid distribution on the face. Cases reported in the literature of multiple spiradenomas are very rare and multiple linear lesions are even rarer. To date, 21 cases of linear/multiple ES have been reported. Of these, eight were in children or adolescents. We report an additional case of this rare clinical presentation and review the literature.