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Embryonal Rhabdomyosarcoma of the Tongue
Author(s) -
Cirocco Antonietta,
González Francisco,
Sáenz Ana María,
Jiménez César,
Sardi José R.,
Oscar Reyes F.
Publication year - 2005
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2005.22308.x
Subject(s) - medicine , embryonal rhabdomyosarcoma , rhabdomyosarcoma , tongue , dermatology , pathology , sarcoma
We report a 10‐month‐old girl who, at 4 months, developed a small, reddish, plaquelike lesion on her tongue. This lesion began to enlarge rapidly, resulting in difficulty in swallowing and breathing. On physical examination, there was a large, red, friable, hard in consistency, irregular tumor over the distal portion of her tongue. The histopathology and immunohistochemical findings were consistent with an embryonal rhabdomyosarcoma. The patient was assigned clinical stage I, group III, and began treatment according to the Intergroup Rhabdomyosarcoma Study guidelines, on triple‐agent chemotherapy consisting of vincristine, actinomycin D, and cyclophosphamide. She only received four cycles because her parents then refused this treatment. After the tumor size was reduced by chemotherapy, a partial anterior glossectomy was performed. After 30 months of follow‐up she has had no recurrences.