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Nevus Psiloliparus and Aplasia Cutis: A Further Possible Example of Didymosis
Author(s) -
Torrelo Antonio,
Boente María del C.,
Nieto Olga,
Asial Raúl,
Colmenero Isabel,
Winik Beatriz,
Zambrano Antonio,
Happle Rudolf
Publication year - 2005
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2005.22305.x
Subject(s) - aplasia cutis congenita , lipomatosis , medicine , scalp , dermatology , nevus , cutis , pathology , melanoma , cancer research
Nevus psiloliparus is a distinct type of mesodermal nevus of the scalp characterized by absence or paucity of hair, and presence of an excessive amount of fatty tissue. It is considered a hallmark of encephalocraniocutaneous lipomatosis, a rare disorder comprising a variety of cutaneous, ophthalmologic, and neurologic defects. We report two infants with encephalocraniocutaneous lipomatosis with nevus psiloliparus on the scalp in close association with aplasia cutis congenita. This unusual association may be considered a further example of didymosis, for which we propose the term, didymosis aplasticopsilolipara.